2 methylsuccinic acid

2-Methylsuccinic acid (Pyrotartaric Acid) is a normal metabolite found in human fluids. Increased urinary levels of 2-Methylsuccinic acid (Pyrotartaric Acid) (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea.

2-Methylsuccinic acid (Standard) is a reference standard for research and analysis in studies involving 2-Methylsuccinic acid. 2-Methylsuccinic acid (Pyrotartaric Acid) is a normal metabolite found in human fluids. Increased urinary levels of 2-Methylsuccinic acid (Pyrotartaric Acid) (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea.

Potassium 2-hydroxy-2-methylsuccinate ((±)-2-Hydroxy-2-methylsuccinic acid dipotassium salt) is a type of endogenous metabolite.

(S)-(-)-Methyl succinic acid is a chiral succinic acid derivative suitable for biochemical experiments and drug synthesis research.