isovaleric acid

Isovaleric acid (Delphinic acid) is a naturally occurring aroma compound found in Bartlett pear brandies, vanilla beans, rape-honey, and banana.

3-Hydroxyisovaleric acid (Beta-Hydroxyisovaleric acid) is an endogenous metabolite excreted in the urine and can serve as an early and sensitive indicator of biotin deficiency.

Isovaleric acid-D9 is a deuterated compound of Isovaleric acid. Isovaleric acid (T5609) has a CAS number of 503-74-2. 3-Methylbutanoic acid is a naturally occurring aroma compound found in Bartlett pear brandies, vanilla beans, rape-honey, and banana.

Isovaleric Acid-D9 (Standard) is a reference standard of Isovaleric Acid-D9 intended for quantitative analysis, quality control, and related biochemical research applications. Isovaleric acid-d9 is a deuterated compound of Isovaleric acid. Isovaleric acid has a CAS number of 503-74-2. 3-Methylbutanoic acid is a naturally occurring aroma compound found in Bartlett pear brandies, vanilla beans, rape-honey, and banana.

3-Hydroxyisovaleric acid (Standard) is a reference standard for research and analysis in studies involving 3-Hydroxyisovaleric acid. 3-Hydroxyisovaleric acid (Beta-Hydroxyisovaleric acid) is an endogenous metabolite excreted in the urine and can serve as an early and sensitive indicator of biotin deficiency.

α-Ketoisovaleric Acid-[D7] Sodium Salt (Standard) is a reference standard of α-Ketoisovaleric Acid-[D7] Sodium Salt intended for quantitative analysis, quality control, and related biochemical research applications.

3-Methyl-2-oxobutanoic acid (2-Oxoisovaleric acid) is an abnormal metabolite that arises from the incomplete breakdown of branched-chain amino acids. 3-Methyl-2-oxobutanoic acid is a neurotoxin, an acidogen, and a metabotoxin. A neurotoxin causes damage to nerve cells and nerve tissues. 3-Methyl-2-oxobutanoic acid is a keto-acid, which is a subclass of organic acids. Abnormally high levels of organic acids in the blood (organic acidemia), urine (organic aciduria), the brain, and other tissues lead to general metabolic acidosis.

2-Hydroxy-3-methylbutyric acid is a structural analog of GHB, a naturally occurring substance found in the central nervous system, and a nootropic.

Increased levels of erucic acid (22:1n9) have been found in the red blood cell membranes of autistic subjects with developmental regression (PMID: 16581239 ). Erucic acid (13(Z)-Docosenoic Acid) is broken down long-chain acyl-coenzyme A (CoA) dehydrogenase, which is produced in the liver. This enzyme breaks this long chain fatty acid into shorter-chain fatty acids. human infants have relatively low amounts of this enzyme and because of this, babies should not be given foods high in erucic acid. Erucic acid is found to be associated with isovaleric acidemia, which is an inborn error of metabolism.

Palmitoleic acid ((Z)-Hexadec-9-enoic acid) is found to be associated with isovaleric acidemia, which is an inborn error of metabolism.

Isovalerylcarnitine (3-methylbutyrylcarnitine) is a small molecule compound produced by the catabolism of L-leucine and the accumulation of isovaleric acid. Isovalerylcarnitine is also a selective and effective calpain activator that can promote cell apoptosis. Isovalerylcarnitine is related to isovaleric acidemia and can be used as a marker of isovaleric acidemia.

Isovaleryl-L-carnitine is a naturally occurring acylcarnitine that is formed via metabolic conversion of L-leucine. It increases survival and decreases apoptosis in hepatocyte growth factor-deprived murine C2.8 hepatocytes when used at a concentration of 1 mM. Isovaleryl-L-carnitine inhibits amino acid deprivation-induced proteolysis and autophagy in isolated perfused rat liver when used at concentrations of 77 and 100 μM, respectively. Increased levels of isovaleryl carnitine are associated with isovaleryl-CoA dehydrogenase deficiency (isovaleric acidemia).

N-Isovaleroylglycine (Isovaleroylglycine) is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However, the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases, the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine. N-Isovaleroylglycine is a byproduct of the catabolism of the amino acid leucine. Accumulation of N-Isovaleroylglycine occurs in Isovaleric Acidemia (IVA).

Pentyl isovalerate is an organic compound belonging to the ester category. Formed from the reaction of pentanol and isovaleric acid, it carries a fruity aroma with subtle floral notes. Pentyl isovalerate finds numerous applications in the flavor and fragrance industry, particularly as a scent component in perfumes, colognes, and air fresheners. Additionally, it serves as a food flavoring agent and as a solvent and plasticizer in industrial settings.

Erucic acid (Standard) is the standard substance of Erucic acid, and it is applicable for quantitative analysis, quality control, and related research in biochemical experiments. Increased levels of erucic acid (22:1n9) have been found in the red blood cell membranes of autistic subjects with developmental regression (PMID: 16581239 ). Erucic acid (13(Z)-Docosenoic Acid) is broken down long-chain acyl-coenzyme A (CoA) dehydrogenase, which is produced in the liver. This enzyme breaks this long chain fatty acid into shorter-chain fatty acids. human infants have relatively low amounts of this enzyme and because of this, babies should not be given foods high in erucic acid. Erucic acid is found to be associated with isovaleric acidemia, which is an inborn error of metabolism.

N-Isovaleroylglycine (Standard) is a reference standard for research and analysis in studies involving N-Isovaleroylglycine. N-Isovaleroylglycine (Isovaleroylglycine) is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However, the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases, the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine. N-Isovaleroylglycine is a byproduct of the catabolism of the amino acid leucine. Accumulation of N-Isovaleroylglycine occurs in Isovaleric Acidemia (IVA).

Ethyl 2-methylpentanoate is classified as an ester and is formed by the esterification of branched isovaleric acid with ethanol. This compound has a fruity and pungent odor and is commonly used as a flavoring agent in baked goods, dairy products, and beverages. It also serves as a fragrance component in personal care products, and as a solvent or plasticizer in various industrial applications. Additionally, ethyl 2-methylpentanoate can be used as a starting material for synthesizing other organic compounds.