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3amino2methylpropanoic acid

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3-Amino-2-methylpropanoic acid
α-Methyl-β-alanine, DL-3-AMINOISOBUTYRIC ACID
T4887144-90-1
3-Amino-2-methylpropanoic acid (α-Methyl-β-alanine) is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6), the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.
  • $29
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3-Amino-2-methylpropanoic acid (Standard)
TMSM-3645144-90-1
3-Amino-2-methylpropanoic acid (Standard) is a reference standard for research and analysis in studies involving 3-Amino-2-methylpropanoic acid. 3-Amino-2-methylpropanoic acid (α-Methyl-β-alanine) is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6), the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.
  • $115
7-10 days
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