l-homocitrulline

L-Homocitrulline (Homocitrulline) is a metabolite that can be detected in larger amounts in the urine of individuals with urea cycle disorders. The accumulation of carbamyl phosphate due to a depleted supply of ornithine for the urea cycle may be responsible for the enhanced synthesis of L-Homocitrulline and homoarginine in some cases.

L-Homocitrulline-D3 is the deuterated form of L-Homocitrulline. In the urea cycle pathway, L-Homocitrulline (T5257) is metabolized into homoarginine by converting homoargininosuccinate. Metabolic irregularities involving L-Homocitrulline (T5257) can result in lysinuric protein intolerance (LPI).

L-Homocitrulline (Standard) is a reference standard for research and analysis in studies involving L-Homocitrulline. L-Homocitrulline (Homocitrulline) is a metabolite that can be detected in larger amounts in the urine of individuals with urea cycle disorders. The accumulation of carbamyl phosphate due to a depleted supply of ornithine for the urea cycle may be responsible for the enhanced synthesis of L-Homocitrulline and homoarginine in some cases.

L-Homocitrulline-2,6,6-[D3] (Standard) is a reference standard of L-Homocitrulline-2,6,6-[D3] intended for quantitative analysis, quality control, and related biochemical research applications.