Powder: -20°C for 3 years | In solvent: -80°C for 1 year
2-Methylsuccinic acid (Pyrotartaric Acid) is a normal metabolite found in human fluids. Increased urinary levels of 2-Methylsuccinic acid (Pyrotartaric Acid) (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea.
Pack Size | Availability | Price/USD | Quantity |
---|---|---|---|
1 g | In stock | $ 29.00 | |
1 mL * 10 mM (in DMSO) | In stock | $ 29.00 |
Description | 2-Methylsuccinic acid (Pyrotartaric Acid) is a normal metabolite found in human fluids. Increased urinary levels of 2-Methylsuccinic acid (Pyrotartaric Acid) (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea. |
Synonyms | Pyrotartaric Acid, Methylbutanedioic acid |
Molecular Weight | 132.115 |
Formula | C5H8O4 |
CAS No. | 498-21-5 |
Powder: -20°C for 3 years | In solvent: -80°C for 1 year
DMSO: 200 mM
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2-Methylsuccinic acid 498-21-5 Metabolism Others Endogenous Metabolite Inhibitor inhibit 2 Methylsuccinic acid 2Methylsuccinic acid Pyrotartaric Acid Methylbutanedioic acid inhibitor