Shopping Cart
Remove All
  • TargetMol
    Your shopping cart is currently empty

Anti-PDHB Antibody (9C498)

(Synonyms: Pyruvate dehydrogenase E1 component subunit beta, mitochondrial, PHE1B, PDHE1-B, PDHB, mitochondrial) Copy Product Info
🥰Excellent

Synonyms: Pyruvate dehydrogenase E1 component subunit beta, mitochondrial, PHE1B, PDHE1-B, PDHB, mitochondrial

Catalog No. TMAC-03480 Copy Product Info
🥰Excellent
Anti-PDHB Antibody (9C498) is a Rabbit antibody targeting PDHB. Anti-PDHB Antibody (9C498) can be used in FCM,IHC,IP,WB.
Anti-PDHB Antibody
(9C498)
Pack SizePriceUSA StockGlobal StockQuantity
50 μL$2967-10 days7-10 days
100 μL$4967-10 days7-10 days
For In stock only · Estimated delivery: USA Stock (1-2 days) Global Stock (5-7 days)
Add to Cart
Add to Quotation
For research use only—not for human use. No sales to individuals. Use as intended only.
Questions
TargetMol
View More

Product Introduction

Bioactivity
Description
Anti-PDHB Antibody (9C498) is a Rabbit antibody targeting PDHB. Anti-PDHB Antibody (9C498) can be used in FCM,IHC,IP,WB.
SynonymsPyruvate dehydrogenase E1 component subunit beta, mitochondrial, PHE1B, PDHE1-B, PDHB, mitochondrial
Ig Type
IgG
Clone
9C498
Reactivity
Human,Mouse,Rat
Application
Recommended Dose
WB: 1:500-2000; IHC: 1:50-200; FCM: 1:50-100
Antibody Type
Monoclonal
Host SpeciesRabbit
ConstructionRecombinant Antibody
PurificationProA affinity purified
AppearanceLiquid
Formulation1*TBS (pH7.4), 1%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide.
Research BackgroundThe pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO. It contains multiple copies of three enzymatic components: pyruvate dehydrogenase (E1), dihydrolipoamide acetyltransferase (E2) and lipoamide dehydrogenase (E3). Defects in PDHB are a cause of pyruvate dehydrogenase E1 component deficiency (PDHE1 deficiency). PDHE1 deficiency is the most common enzyme defect in patients with primary lactic acidosis. It is associated with variable clinical phenotypes ranging from neonatal death to prolonged survival complicated by developmental delay, seizures, ataxia, apnea, and in some cases to an X-linked form of Leigh syndrome (LS) (Leigh encephalomyelopathy).
Related Conjugates and Formulations
Conjucates
Unconjugated
Antigen Details
Immunogen
Recombinant Protein
Uniprot ID
Chemical Properties
Stability & Storage
Stability & StorageStore at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles.
TransportShipping with blue ice.

Calculator

  • Dilution Calculator
  • Reconstitution Calculator

Keywords

Related Tags: