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Anti-Dysferlin Antibody (4C391)

(Synonyms: MMD1, MM, Miyoshi myopathy, Limb girdle muscular dystrophy 2B (autosomal recessive), Limb girdle muscular dystrophy 2B, LGMD2B, LGMD 2B, FLJ90168, FLJ00175, Fer-1-like protein 1, FER1L1, Fer1 like protein 1, Fer 1 like protein 1, Dystrophy-associated fer-1-like protein, Dystrophy associated fer1 like protein, Dystrophy associated fer1 like 1, Dystrophy associated fer 1 like protein, Dystrophy associated fer 1 like 1, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive), Dysferlin limb girdle muscular dystrophy 2B, Dysferlin, DYSF_HUMAN, DYSF, DMAT) Copy Product Info
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Synonyms: MMD1, MM, Miyoshi myopathy, Limb girdle muscular dystrophy 2B (autosomal recessive), Limb girdle muscular dystrophy 2B, LGMD2B, LGMD 2B, FLJ90168, FLJ00175, Fer-1-like protein 1, FER1L1, Fer1 like protein 1, Fer 1 like protein 1, Dystrophy-associated fer-1-like protein, Dystrophy associated fer1 like protein, Dystrophy associated fer1 like 1, Dystrophy associated fer 1 like protein, Dystrophy associated fer 1 like 1, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive), Dysferlin limb girdle muscular dystrophy 2B, Dysferlin, DYSF_HUMAN, DYSF, DMAT

Catalog No. TMAC-01203 Copy Product Info
🥰Excellent
Anti-Dysferlin Antibody (4C391) is a Rabbit antibody targeting Dysferlin. Anti-Dysferlin Antibody (4C391) can be used in ICC/IF,IHC,WB.
Anti-Dysferlin Antibody
(4C391)
Pack SizePriceUSA StockGlobal StockQuantity
50 μL$2977-10 days7-10 days
100 μL$4977-10 days7-10 days
For In stock only · Estimated delivery: USA Stock (1-2 days) Global Stock (5-7 days)
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For research use only—not for human use. No sales to individuals. Use as intended only.
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Product Introduction

Bioactivity
Description
Anti-Dysferlin Antibody (4C391) is a Rabbit antibody targeting Dysferlin. Anti-Dysferlin Antibody (4C391) can be used in ICC/IF,IHC,WB.
SynonymsMMD1, MM, Miyoshi myopathy, Limb girdle muscular dystrophy 2B (autosomal recessive), Limb girdle muscular dystrophy 2B, LGMD2B, LGMD 2B, FLJ90168, FLJ00175, Fer-1-like protein 1, FER1L1, Fer1 like protein 1, Fer 1 like protein 1, Dystrophy-associated fer-1-like protein, Dystrophy associated fer1 like protein, Dystrophy associated fer1 like 1, Dystrophy associated fer 1 like protein, Dystrophy associated fer 1 like 1, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive), Dysferlin limb girdle muscular dystrophy 2B, Dysferlin, DYSF_HUMAN, DYSF, DMAT
Ig Type
IgG
Clone
4C391
Reactivity
Human,Mouse
Application
Recommended Dose
WB: 1:1000-2000; IHC: 1:100-200; ICC/IF: 1:50-200
Antibody Type
Monoclonal
Host SpeciesRabbit
ConstructionRecombinant Antibody
PurificationAffinity-chromatography
AppearanceLiquid
FormulationRabbit IgG in 10mM phosphate buffered saline , pH 7.4, 150mM sodium chloride, 0.05% BSA, 0.02% sodium azide and 50% glycerol.
Research BackgroundKey calcium ion sensor involved in the Ca2+-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress.
Related Conjugates and Formulations
Conjucates
Unconjugated
Antigen Details
Immunogen
A synthesized peptide: human Dysferlin
Antigen Species
Human
Uniprot ID
Chemical Properties
Molecular WeightTheoretical: 237 kDa.
Stability & Storage
Stability & StorageStore at 2°C-8°C for 1 month. Store at -20°C or -80°C for 12 months. Avoid repeated freeze-thaw cycles.
TransportShipping with blue ice.

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